Abstract
We report a case of vanishing gastroschisis visualized by antenatal ultrasound with
a 7-year long term follow-up. Currently, the child is still dependent on daily parenteral
nutrition with no signs of hepatotoxicity. To our knowledge, it’s the fourth case
with a long-term follow-up. Vanishing gastroschisis is a rare complication of gastroschisis.
However, physicians should be aware of it because its prognosis is worse than classical
gastroschisis. When a vanishing gastroschisis is visualized or suspected by antenatal
ultrasound, prenatal counseling is required with explanations about the risk of short
bowel syndrome, the need of parenteral nutrition and related complications (inflammatory
colitis, sepsis, liver failure and organ transplant). Mortality rate was initially
around 93%, and dropped to 27% after the years 2000 (versus 10% for classical gastroschisis).
After birth, all children will require surgery, and sometimes autologous gastro-intestinal
reconstruction. Most survivors (68%) could be taken off the TPN. Unfortunately, long-term
outcomes for children with vanishing gastroschisis are still missing in current literature.
Keywords
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Article info
Publication history
Published online: June 19, 2018
Accepted:
June 13,
2018
Received:
May 23,
2018
Identification
Copyright
© 2018 Elsevier B.V. All rights reserved.
