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Letter| Volume 283, P169-170, April 2023

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Fetal intrahepatic portosystemic shunts: A benign and self-limiting feature?

  • Li Zhen
    Affiliations
    Prenatal Diagnostic Center, Guangzhou Women and Children’s Medical Center affiliated to Guangzhou Medical University, Guangzhou, Guangdong, China
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  • Xiao-Mei Lin
    Affiliations
    Prenatal Diagnostic Center, Guangzhou Women and Children’s Medical Center affiliated to Guangzhou Medical University, Guangzhou, Guangdong, China
    Search for articles by this author
  • Dong-Zhi Li
    Correspondence
    Corresponding author at: Jinsui Road 9, Zhujiang New Town, Guangzhou, Guangdong 510623, China.
    Affiliations
    Prenatal Diagnostic Center, Guangzhou Women and Children’s Medical Center affiliated to Guangzhou Medical University, Guangzhou, Guangdong, China
    Search for articles by this author
Published:February 14, 2023DOI:https://doi.org/10.1016/j.ejogrb.2023.02.010
      Congenital portosystemic shunts (PSS) are vascular malformations creating abnormal connections between portal and systemic veins. Blood collected from digestive organs is shunted to the systemic circulation, resulting in possible adverse consequence. There are two categories of congenital shunts, extrahepatic (EPSS) and intrahepatic (IPSS). Current data indicates that IPSS has a favorable prognosis [
      • Papamichail M.
      • Pizanias M.
      • Heaton N.
      Congenital portosystemic venous shunt.
      ]. However, previous studies were mainly based on findings of neonatal patients. We present the pregnancy and postnatal outcomes of sixteen fetal cases of IPSS. This knowledge will help assess the possible clinical impact, parental counseling, and perinatal management.
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